Autoimmune hepatitis (AIH) is a chronic progressive liver disease leading to end-stage liver disease and/or death, if left untreated [1–3]. Within the spectrum of AIH, some patients exhibiting characteristics of primary biliary cholangitis (PBC) or primary sclerosing cholangitis (PSC) are classified as variant forms of AIH [1–4]. The prevalence of AIH/PBC variant is generally considered to be about 10% of adult patients with AIH or PBC [4,5]. The ``Paris criteria'' are the most widely used diagnostic tools for the definition of AIH/PBC variant [6].
