Cerebral venous thrombosis (CVT) is a rare cause of stroke and intracranial hypertension syndrome. Compared to arterial stroke, CVT affects younger people, predominantly women, has a different risk factors profile, and a subtle and multiform clinical presentation. Risk factors include pregnancy and puerperium, oral contraceptives, inherited thrombophilia, malignancy, infections, obesity, diagnostic and treatment procedures. The wide spectrum of clinical presentations make the diagnosis difficult.