Abdominal aortic aneurysms (AAA) affect approximately 5 % of male over the age of 65 [1]. Among these, 5 % to 10 % are classified as inflammatory AAA (IAAA) [2]. A wide range of underlying aetiologies has been identified [3–5], including idiopathic forms, large vessel vasculitis (LVV), IgG4-related disease (IgG4-RD), infectious origins, or haematological disorders. The aim of this study was to describe the clinical and radiological phenotypes of IAAA based on their aetiology and to describe long-term outcome.