Eosinophilic granulomatosis with polyangiitis (EGPA), formerly known as Churg-Strauss syndrome [1], is a systemic vasculitis classified as an anti-neutrophil cytoplasm antibody (ANCA)-associated vasculitis (AAV) [1–3]. EGPA is a rare disease with an annual global incidence rate of 1.7 cases per million people per year and a prevalence of 15.6 cases per million people [4]. It arises during the 4th to 6th decade of life, with an average age at diagnosis of 49 years, although paediatric cases have also been reported.
